• A16AA Amino acids and derivatives 16 drugs
• A16AB Enzymes 21 drugs
• A16AX Various alimentary tract and metabolism products 40 drugs

Drugs with code A16A

• ALDURAZYME, 100 U/ML CONCENTRATE FOR SOLUTION FOR INFUSION

  Form: solution for infusion, concentrate

  Active substance	Dosage
  laronidase	100 U

  ATC code: A16A, A16AB, A16AB05

  Manufacturer: Sanofi B.V.

• AMMONAPS 500 MG TABLETS

  Form: tablets

  Active substance	Dosage
  sodium phenylbutyrate	500 mg

  ATC code: A16A, A16AX, A16AX03

  Manufacturer: Immedica Pharma Ab

• BRINEURA 150 MG SOLUTION FOR INFUSION

  Form: solution for infusion

  Active substance	Dosage
  cerliponase alfa	150 mg/ml

  ATC code: A16A, A16AB, A16AB17

  Manufacturer: Biomarin International Limited

• CARBAGLU 200 MG DISPERSIBLE TABLETS

  Form: tablets, dispersible

  Active substance	Dosage
  carbamoylglutamic acid	200 mg

  ATC code: A16A, A16AA, A16AA05

  Manufacturer: Recordati Rare Diseases

• CARBAGLU 200 MG DISPERSIBLE TABLETS

  Form: tablets, dispersible

  Active substance	Dosage
  carbamoylglutamic acid	200 mg

  ATC code: A16A, A16AA, A16AA05

  Manufacturer: Recordati Rare Diseases

• CARGLUMIC ACID WAYMADE 200 MG DISPERSIBLE TABLETS EFG

  Form: tablets, dispersible

  Active substance	Dosage
  carbamoylglutamic acid	200 mg

  ATC code: A16A, A16AA, A16AA05

  Manufacturer: Waymade B.V.

• CARNICOR 100 MG/ML ORAL SOLUTION

  Form: solution, oral

  Active substance	Dosage
  l-carnitine	1 g

  ATC code: A16A, A16AA, A16AA01

  Manufacturer: Alfasigma Espana S.L.

• CARNICOR 200 MG/ML SOLUTION FOR INJECTION

  Form: solution for injection

  Active substance	Dosage
  l-carnitine	1000 mg

  ATC code: A16A, A16AA, A16AA01

  Manufacturer: Alfasigma Espana S.L.

• CARNICOR 300 MG/ML ORAL SOLUTION

  Form: solution, oral

  Active substance	Dosage
  l-carnitine	1,5 g

  ATC code: A16A, A16AA, A16AA01

  Manufacturer: Alfasigma Espana S.L.

• CERDELGA 84 MG HARD CAPSULES

  Form: capsules, hard

  Active substance	Dosage
  eliglustat	84 mg

  ATC code: A16A, A16AX, A16AX10

  Manufacturer: Sanofi B.V.

• CEREZYME 400 UNITS POWDER FOR CONCENTRATE FOR SOLUTION FOR INFUSION

  Form: solution for infusion, concentrate

  Active substance	Dosage
  imiglucerase	400 UI

  ATC code: A16A, A16AB, A16AB02

  Manufacturer: Sanofi B.V.

• CRECIL 500 MG HARD CAPSULES

  Form: capsules, hard

  Active substance	Dosage
  cystine	500 mg

  ATC code: A16A, A16AA

  Manufacturer: Laboratorios Vinas S.A.

• CUFENCE 200 MG HARD CAPSULES

  Form: capsules, hard

  Active substance	Dosage
  triethylenetetramine dihydrochloride	300 mg

  ATC code: A16A, A16AX, A16AX12

  Manufacturer: Univar Solutions B.V.

• CUPRIOR 150 MG FILM-COATED TABLETS

  Form: tablets, film-coated

  Active substance	Dosage
  trientine tetrahydrochloride	300 mg

  ATC code: A16A, A16AX, A16AX12

  Manufacturer: Orphalan

• CYSTADANE 1 G ORAL POWDER

  Form: powder for oral solution

  Active substance	Dosage
  anhydrous betaine	1 g

  ATC code: A16A, A16AA, A16AA06

  Manufacturer: Recordati Rare Diseases

• CYSTAGON 150 MG HARD CAPSULES

  Form: capsules, hard

  Active substance	Dosage
  mercaptamine	150 mg

  ATC code: A16A, A16AA, A16AA04

  Manufacturer: Recordati Rare Diseases

• CYSTAGON 50 MG HARD CAPSULES

  Form: capsules, hard

  Active substance	Dosage
  mercaptamine	50 mg

  ATC code: A16A, A16AA, A16AA04

  Manufacturer: Recordati Rare Diseases

• CYSTINE 250 MG TABLETS

  Form: tablets

  Active substance	Dosage
  cystine	250 mg

  ATC code: A16A, A16AA

  Manufacturer: La Quimica Medica S.A.

• ELAPRASE 2 MG/ML CONCENTRATE FOR SOLUTION FOR INFUSION

  Form: solution for infusion, concentrate

  Active substance	Dosage
  idursulfase	2 mg

  ATC code: A16A, A16AB, A16AB09

  Manufacturer: Takeda Pharmaceuticals International Ag Ireland Branch

• ELFABRIO 2 MG/ML CONCENTRATE FOR SOLUTION FOR INFUSION

  Form: solution for infusion, concentrate

  Active substance	Dosage
  peguniglucidase alfa	20 mg

  ATC code: A16A, A16AB, A16AB20

  Manufacturer: Chiesi Farmaceutici S.P.A.

• FABRAZYME 35 MG POWDER FOR CONCENTRATE FOR SOLUTION FOR INFUSION

  Form: powder for concentrate for solution for infusion

  Active substance	Dosage
  agalsidase beta	5 mg

  ATC code: A16A, A16AB, A16AB04

  Manufacturer: Sanofi B.V.

• FABRAZYME 5 MG POWDER FOR CONCENTRATE FOR INFUSION SOLUTION

  Form: powder for concentrate for solution for infusion

  Active substance	Dosage
  agalsidase beta	5 mg

  ATC code: A16A, A16AB, A16AB04

  Manufacturer: Sanofi B.V.

• GALAFOLD 123 MG HARD CAPSULES

  Form: capsules, hard

  Active substance	Dosage
  migalastat hydrochloride	150 mg

  ATC code: A16A, A16AX, A16AX14

  Manufacturer: Amicus Therapeutics Europe Limited

• GIVLAARI 189 MG/ML SOLUTION FOR INJECTION

  Form: solution for injection

  Active substance	Dosage
  givosiran	200 mg/ml

  ATC code: A16A, A16AX, A16AX16

  Manufacturer: Alnylam Netherlands B.V.

• KANUMA 2 MG/ML CONCENTRATE FOR SOLUTION FOR INFUSION

  Form: solution for infusion, concentrate

  Active substance	Dosage
  sebelipase alfa	20 mg

  ATC code: A16A, A16AB, A16AB14

  Manufacturer: Alexion Europe Sas

• KUVAN 100 MG, DISPERSIBLE TABLETS

  Form: tablets

  Active substance	Dosage
  sapropterin	100 mg

  ATC code: A16A, A16AX, A16AX07

  Manufacturer: Biomarin International Limited

• LAMZEDE 10 MG POWDER FOR SOLUTION FOR INFUSION

  Form: powder for solution for infusion

  Active substance	Dosage
  velmanase alpha	10 mg

  ATC code: A16A, A16AB, A16AB15

  Manufacturer: Chiesi Farmaceutici S.P.A.

• LEBERSAL EFFERVESCENT GRANULES ORANGE FLAVOUR

  Form: granules, effervescent

  Active substance	Dosage
  sodium sulfate	3,15 g
  magnesium sulfate	0,99 g
  sodium bicarbonate	39,3 g
  sodium phosphate	8,28 g

  ATC code: A16A, A16AX

  Manufacturer: Laboratorios Ern S.A.

• LIBMELDY 2-10 X 10^6 CELLS/ML DISPERSION FOR INFUSION

  Form: solution for injection

  Active substance	Dosage
  atidarsagen autotemcel	2-10 million células/ml

  ATC code: A16A, A16AB, A16AB21

  Manufacturer: Orchard Therapeutics (Netherlands) B.V.

• LOARGYS 5 MG/ML SOLUTION FOR INJECTION AND FOR INFUSION

  Form: solution for injection and for infusion

  Active substance	Dosage
  pegzilarginase	2 mg

  ATC code: A16A, A16AB, A16AB24

  Manufacturer: Immedica Pharma Ab

• MEPSEVII 2 MG/ML CONCENTRATE FOR SOLUTION FOR INFUSION

  Form: solution for infusion, concentrate

  Active substance	Dosage
  vestronidase alfa	10 mg

  ATC code: A16A, A16AB, A16AB18

  Manufacturer: Ultragenyx Germany Gmbh

• MIGLUSTAT ACCORD 100 MG HARD CAPSULES EFG

  Form: capsules, hard

  Active substance	Dosage
  miglustat	100 mg

  ATC code: A16A, A16AX, A16AX06

  Manufacturer: Accord Healthcare S.L.U.

• MIGLUSTAT DIPHARMA 100 MG HARD CAPSULES EFG

  Form: capsules, hard

  Active substance	Dosage
  miglustat	100 mg

  ATC code: A16A, A16AX, A16AX06

  Manufacturer: Dipharma Arzneimittel Gmbh

• MIGLUSTAT GEN.ORPH 100 MG HARD CAPSULES EFG

  Form: capsules, hard

  Active substance	Dosage
  miglustat	100 mg

  ATC code: A16A, A16AX, A16AX06

  Manufacturer: Gen.Orph S.A.S.

• MYOZYME 50 MG CONCENTRATE FOR SOLUTION FOR INFUSION

  Form: powder for concentrate for solution for infusion

  Active substance	Dosage
  alglucosidase alfa	50 mg

  ATC code: A16A, A16AB, A16AB07

  Manufacturer: Sanofi B.V.

• NAGLAZYME 1 MG/ML CONCENTRATE FOR INFUSION SOLUTION

  Form: solution for injection

  Active substance	Dosage
  galsulfase	1 mg

  ATC code: A16A, A16AB

  Manufacturer: Biomarin International Limited

• NEXVIADYME 100 MG POWDER FOR CONCENTRATE FOR SOLUTION FOR INFUSION

  Form: powder for concentrate for solution for infusion

  Active substance	Dosage
  avalglucosidase alfa	10 mg/ml

  ATC code: A16A, A16AB, A16AB22

  Manufacturer: Sanofi B.V.

• NITISINONE DIPHARMA 10 MG HARD CAPSULES EFG

  Form: capsules, hard

  Active substance	Dosage
  nitisinone	10 mg

  ATC code: A16A, A16AX, A16AX04

  Manufacturer: Dipharma Arzneimittel Gmbh

• NITISINONE DIPHARMA 2 MG HARD CAPSULES EFG

  Form: capsules, hard

  Active substance	Dosage
  nitisinone	2 mg

  ATC code: A16A, A16AX, A16AX04

  Manufacturer: Dipharma Arzneimittel Gmbh

• NITISINONE DIPHARMA 20 MG HARD CAPSULES EFG

  Form: capsules, hard

  Active substance	Dosage
  nitisinone	20 mg

  ATC code: A16A, A16AX, A16AX04

  Manufacturer: Dipharma Arzneimittel Gmbh

• NITISINONE DIPHARMA 5 MG HARD CAPSULES EFG

  Form: capsules, hard

  Active substance	Dosage
  nitisinone	5 mg

  ATC code: A16A, A16AX, A16AX04

  Manufacturer: Dipharma Arzneimittel Gmbh

• NITISINONE MDK 10 MG HARD CAPSULES

  Form: capsules, hard

  Active substance	Dosage
  nitisinone	10 mg

  ATC code: A16A, A16AX, A16AX04

  Manufacturer: Mendelikabs Europe Limited

• NITISINONE MDK 2 MG HARD CAPSULES

  Form: capsules, hard

  Active substance	Dosage
  nitisinone	2 mg

  ATC code: A16A, A16AX, A16AX04

  Manufacturer: Mendelikabs Europe Limited

• NITISINONE MDK 5 MG HARD CAPSULES

  Form: capsules, hard

  Active substance	Dosage
  nitisinone	5 mg

  ATC code: A16A, A16AX, A16AX04

  Manufacturer: Mendelikabs Europe Limited

• OPFOLDA 65 MG HARD CAPSULES

  Form: capsules, hard

  Active substance	Dosage
  miglustat	65 mg

  ATC code: A16A, A16AX, A16AX06

  Manufacturer: Amicus Therapeutics Europe Limited

• ORFADIN 10 MG HARD CAPSULES

  Form: capsules, hard

  Active substance	Dosage
  nitisinone	10 mg

  ATC code: A16A, A16AX, A16AX04

  Manufacturer: Swedish Orphan Biovitrum International Ab

• ORFADIN 2 MG HARD CAPSULES

  Form: capsules, hard

  Active substance	Dosage
  nitisinone	2 mg

  ATC code: A16A, A16AX, A16AX04

  Manufacturer: Swedish Orphan Biovitrum International Ab

• ORFADIN 20 MG HARD CAPSULES

  Form: capsules, hard

  Active substance	Dosage
  nitisinone	20 mg

  ATC code: A16A, A16AX, A16AX04

  Manufacturer: Swedish Orphan Biovitrum International Ab

• ORFADIN 4 MG/ML ORAL SUSPENSION

  Form: suspension, oral

  Active substance	Dosage
  nitisinone	4,0 mg

  ATC code: A16A, A16AX, A16AX04

  Manufacturer: Swedish Orphan Biovitrum International Ab

• ORFADIN 5 MG HARD CAPSULES

  Form: capsules, hard

  Active substance	Dosage
  nitisinone	5 mg

  ATC code: A16A, A16AX, A16AX04

  Manufacturer: Swedish Orphan Biovitrum International Ab